GATA2 mutations in sporadic and familial acute myeloid leukaemia patients with CEBPA mutations

Br J Haematol. 2013 Jun;161(5):701-705. doi: 10.1111/bjh.12317. Epub 2013 Apr 5.

Abstract

GATA2 mutations have recently been reported in acute myeloid leukaemia (AML) patients with CEBPA-double mutations. To explore their impact on this favourable-risk disease, we determined GATA2 status in 153 sporadic AML patients and three members of a germ-line CEBPA-mutant family at AML presentation. Overall, 27% (15/55) CEBPA-double, 16% (7/43) CEBPA-single and 0% (0/55) normal karyotype/CEBPA-wild-type patients were GATA2-mutant. All familial AML patients acquired both a second CEBPA and a GATA2 mutation. CEBPA and GATA2 mutant levels indicated that both mutations were likely to be early events in leukaemogenesis. GATA2 status did not impact on the favourable outcome of CEBPA-double/FLT3-inernal tandem duplication-negative patients.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • CCAAT-Enhancer-Binding Proteins / genetics*
  • Female
  • GATA2 Transcription Factor / genetics*
  • Germ-Line Mutation
  • Humans
  • Kaplan-Meier Estimate
  • Leukemia, Myeloid, Acute / genetics*
  • Male
  • Middle Aged
  • Mutation*
  • Neoplasm Proteins / genetics
  • Pedigree
  • Prognosis
  • Treatment Outcome
  • Young Adult

Substances

  • CCAAT-Enhancer-Binding Proteins
  • CEBPA protein, human
  • GATA2 Transcription Factor
  • GATA2 protein, human
  • Neoplasm Proteins